Hemophilia - mece ce, da kuma yadda za a kauce wa rikitarwa mai tsanani?

Yi la'akari da hemophilia - cewa wannan yana da matukar muhimmanci, saboda wannan rashin lafiya ne. Wannan farfadowa shine haɗin kai. Wannan cuta yana da matukar hatsari: yana da mahimmanci a gane shi a matakin farko na ci gaban, don kada ya kawo yanayin zuwa wani mummunar yanayi.

Hemophilia - menene?

Don gane abin da wannan rashin lafiya yake, ma'anar kalmar da ake amfani da ita zai taimaka. Daga harshen Helenanci, "haima" na nufin "jini," da "philia" na nufin "jaraba". Wannan cuta ne halin low jini coagulability. Suna sha wahala daga mutane, amma akwai wasu (misali C). Suna samun mummunan jini daga cikin mahaifiyarta: ita ce mai dauke da cutar kuma tana canja '' '' '' '' '' '' '' '' '' '' ya'yanta. Tarihin ya ƙunshi sunayen manyan mata waɗanda ke ɗauke da kwayar hemophilia. Alal misali, Sarauniya Victoria da Duchess na Hesse.

Yaya aka samu haemophilia?

Harshen wannan farfadowa ba shi da tushe. An samo shi a cikin X chromosome. Gidaran jinsin mahaifa yana hade da jima'i. Domin fara nuna cutar, kana bukatar biyu X-chromosomes tare da maye gurbin. Wannan mace ce "saita". Maza suna da X da Y chromosomes. Duk da haka, a aikace duk abin ya faru daban. Lokacin da mace ta yi juna biyu tare da yarinya wanda ke ɗauke da X-chromosomes guda biyu, tozarta yakan faru ne na tsawon makonni hudu. Wannan shi ne saboda gaskiyar cewa tayin tayi ba zai iya yiwuwa ba.

Yarinya za a iya haife shi tare da maye gurbin X chromosome. A wannan yanayin, cutar kanta ba ta nuna kanta ba: jinsin lafiya mai rinjaye ba ya jawo hankalin magungunan cutar. Abokan gādo na hemophilia za a iya kiyaye su cikin yara. A cikin jiki namiji, babu wani jigon jini a cikin Y-chromosome, kuma X-saitin tare da maye gurbi yana ci gaba sosai. Saboda haka, yara sukan sami wannan cuta, kuma hemophilia yana da ma'ana.

Menene ya haddasa mummunan jini?

Wannan yanayin rashin lafiyar yana da hatsarin gaske. Sakamakon matsalolin da ke gaba yana danganta da mataki na cutar. Wannan shi ne yadda haɗari da mummunan aiki na jini shine:

1. Yana haifar da cirewa daga cikin mahaifa cikin marigayi.
2. Zai iya haifar da zub da jini lokacin aiki.
3. Rashin hawan ƙwayoyi, ƙwayar ƙwayar cuta da kuma raunuka mai tsanani ya jawo hadarin jini.

Hemophilia - Dabbobi

Yin zubar da jini yana da kariya daga jiki. A wannan tsari, fibrinogens, platelets da dalilan plasma suna taka rawar gani. Rashin ɗayan ɗaya daga cikin waɗannan abubuwa yana haifar da rushewa a cikin aiki na tsarin tsarin haɗin gwiwa. Dangane da ɓataccen ɓangaren, waɗannan nau'o'in hemophilia suna bambanta:

• A;
• B;
• C.

Bisa ga mahimmancin irin wannan cuta, wadannan nau'o'in ilimin lissafi sun bambanta:

1. Mai sauƙi - tare da zub da jini yana da wuya. Bugu da ƙari, suna da rauni.
2. Matsayi mai tsanani - saboda halin yana nuna rashin daidaituwa na bayyanar basira.
3. Mai tsanani - idan, alal misali, rashin hakar jini a cikin jariri, wannan yana bayyana ta zub da jini daga igiya mai mahimmanci, gabanin hematomas a kan kai, da miya da sauransu. A lokacin da aka girma, irin wannan cuta ba ta da hatsari fiye da lokacin haihuwa.

Hemophilia A

Ga irin wannan cutar ne halin da kasawa na antihemophilic globulin - factor VIII. Irin wannan rashin lafiya ana dauke da classic kuma mafi yawancin. An gano shi a cikin kashi 85% na lokuta yayin da mai haɗarin yana da kwayar cutar hemophilia. Irin wannan cuta yana tare da jini mai tsanani. Saboda wannan dalili yana da mahimmanci mu fahimci: hemophilia - mece ce da abin da ke damuwa da.

Sakamakon bambancin irin wannan ciwo shine cin zarafin lokacin plasma na hemostasis. A cikin sauƙi, zub da jini ba yakan faru ba da zarar sun ji rauni. Wannan shi ne saboda platelet da gyaran ƙwayoyin cuta suna da kyau. Bayan wannan rana bayan da aka samu rauni, zubar da jinin zai iya farawa, wanda yake da wuya a dakatar. Wannan matsala ba za'a iya warwarewa a rana daya ba.

Hemophilia B

Sunan na biyu don wannan cuta shine cutar Christmass. Haka kuma cutar tana da rashi na factor IX. Wannan ƙungiyar enzyme ta kunna maɗaurin Stuart-Prower. Irin wannan nakasar a cikin yara yana faruwa a cikin kashi 20 cikin dari na ƙwayoyin cuta tare da ganewar asali na coagulability mai rauni. Irin wannan alamun an gano a cikin 1 daga cikin yara 30,000.

Hemophilia C

Wannan tallace-tallace yana da nasawar bayyanar asibiti. Ya bambanta da irin nau'in cuta. Wadannan takaddun ma an cire su daga tsarawar zamani. Saboda wannan dalili yana da mahimmanci don fahimtar hemophilia - menene shi. Yana da siffar da ba ta faruwa a wasu nau'in cutar. Irin wannan birifa a cikin mata ana kiyayewa sau da yawa kamar yadda maza. Wannan shi ne saboda gaskiyar cewa canja wurin ginin yana gudana ta hanyar jigogi. Har ila yau, akwai yiwuwar kasa a jihar. Wannan cuta tana rinjayar Yahudawa da yawa daga Ashkenazi.

Alamun hemophilia

A cikin cututtuka na nau'ikan A da B, wani hoto mai kama da juna. A wannan yanayin, talauci mai yalwacin jini yana haifar da bayyanar cututtuka kamar haka:

1. Kasancewar daban-daban hematomas a jiki. Suna bayyana ko da bayan karamin ƙuƙwalwa. Wadannan hematomas suna da nau'in rarraba. Lokacin da ake dannawa a kan wurin kurkuku akwai ciwo mai tsanani.
2. A cikin 80% na lokuta, hemarthrosis na faruwa. Haɗin gwiwa ya zama mummunan zafi, zafi, kuma fatar jiki a jikinsa ya zama blushes. Tare da maimaita hemorrhages, osteoarthritis fara ci gaba. A lokaci ɗaya tare da shi za'a iya samun ƙananan kasusuwa da kasusuwa da ƙananan kwaskwarima, ƙwayar tsokoki, ƙazantar ƙafa.
3. Gurasar da ke faruwa a bayan tiyata, cututtuka, hakar hakori da sauran raunuka.
4. A cikin kashi 5 cikin dari (lokuta mafi yawa a cikin marasa lafiya a lokacin ƙuruciyar) akwai fashewa mai kwakwalwa .
5. Raunin jini a cikin zubar da jini - yana tare da ciwo mai tsanani da sauran alamu kamar na asibiti na peritonitis.
6. A cikin kashi 20 cikin dari, an lura da hematuria. Wannan yanayin ilimin cututtuka na iya zama tare da hare-haren ƙwayar kullun kuma ya haifar da ci gaban pyelonephritis.
7. Gabatarwar gangrene , wanda haɗarin hematomas ya haɗu.
8. Cutar zubar da jini, wadda aka lura a cikin kashi 8 cikin dari na lokuta a cikin waɗanda ke shan wahala daga matalauta. Ƙananan sauƙi sukan kasance tare da rashin ƙarfi da rashin hankali.

Alamar rashin jinin jinin jini a cikin yanayin hawan Halifa a C mafi yawancin marasa lafiya an bayyana shi a fili ko ba a bayyana ba. Wasu mutane suna da zub da jini, zubar da jini da bayyanar cutar kan jiki. Koda a cikin iyali ɗaya, wanda mambobinsa ke shan wahala daga wannan ciwo, yawancin bayyanar da ke cikin asibiti ya bambanta sosai. Duk da haka, ba kamar cututtuka na iri A da B, hemophilia C bazuka kwatsam a cikin tsokoki suna da wuya. Hemarthroses yakan faru ne kawai a yanayin rikici na haɗin gwiwa.

Bad coagulability na jini - abin da ya yi?

Idan kana da akalla alama ɗaya daga cikin cutar, ya kamata ka nemi taimakon likita nan da nan. Don tabbatar da ganewar asali, likita zai rubuta wa jarrabawa binciken wanda ya hada da irin wadannan hanyoyin dabarun:

• ƙaddarar yawan yawan abubuwan coagulation da ke cikin jini;
• Alamar shafi
• tabbatarwa na lokacin lokacin da jini clotting faruwa;
• Daidaita;
• matakin fibrogen cikin jini da sauransu.

An yi la'akari da Hemophilia ba mahimmanci - maganin wannan cututtukan ya rage zuwa farfadowa na farfadowa. Bugu da ƙari, ba a taka muhimmiyar rawa ba ga abinci mai gina jiki. Yayin da za'a tabbatar da wannan cututtuka, dole ne a gudanar da magani a asibiti na likita. Masana irin wannan likita san hemophilia - abin da pathology shi ne. Mai haƙuri wanda ya tuntubi mai haƙuri ya kasance yana da "Littafin mai haƙuri" tare da shi. Wannan rubutun da ke biye yana dauke da bayanin game da jini jini, da nauyin Rh. Har ila yau, yana nuna tsananin cutar.

Yaya za a dakatar da jinin tare da zubar da jini marar kyau?

Lokacin da mutum yana da halifa, yana bukatar ya zama mai hankali sosai. Ba za ku iya ɗaukar lafiyar lafiyar ku ba! Ka'idojin hali a wannan yanayin sune kamar haka:

1. Idan raunuka sunyi zurfi, kana buƙatar ɗauka da kuma yin sauyawa. Bugu da ƙari, a yi amfani da kankara zuwa wurin da aka lalace (kada ya kasance cikin hulɗa da fata, don haka dole ne a nannade shi da tawul na takarda ko tawul din da aka yi amfani da ita kafin amfani).
2. A cikin rauni da scratches iya samar da manyan clots. Daga gare su, jinin ya ƙone. Saboda irin wannan clots, raunuka ƙara. Don kauce wa wannan, kana buƙatar ka cire "lumps" a hankali. Bugu da ari, wannan yankin ya kamata a wanke tare da bayani na penicillin. Bayan haka, wani takalma wanda aka yi amfani da shi da abun da ke cikin hemostatic ya shafi fata. Wannan accelerates warkar da rauni.

Magunguna tare da karancin jini coagulability

Far for hemophilia kama da wannan:

1. Mai haƙuri yana allurar da abubuwan da suka ɓace. Yawan waɗannan hanyoyi na iya bambanta daga 4 zuwa 8 kowace rana.
2. Sanya kayan injections na shirye-shirye da aka yi a kan plasma.
3. Don cire daga cututtukan jikin marasa lafiya zuwa abubuwan haɓaka, likita zai iya rubuta plasmapheresis .
4. Haɗin haɗin gizon da aka ba da kyauta yana samar da wani bayani na glucose, Reamberin ko Polyglucin.

Tare da hemarthroses, ana yin ƙarin fashewa na jakar jigilar. Zuciyar kayan ciki na jini da kuma wadatawa tare da shirye-shirye na hormonal da aka gudanar. Ba tare da yakamata ba, an kamata a yi wa yankakken da aka shafi a lokacin farfadowa. A nan gaba, bayan an tsabtace su, an ba da horo ga ilimin jiki da aikin likita.

Abin da za ku ci tare da rashin jinin jini clotting?

Gina na gina jiki yana da karfi a kan yanayin marasa lafiya. Don hana abin da ke faruwa na zub da jini, marasa lafiya da hemophilia zasu wadata abincin su tare da irin wannan abinci:

• ƙwayoyin dabba (man shanu, man alade, cream);
• hanta (ƙwayar zuciya, kodan, hanta);
• buckwheat porridge;
• berries na violet launi (blueberry, blueberry, blackberry da sauransu);
• ayaba da mangoes;
• jan barkono, radish, jan kabeji da sauran kayan lambu;
• walnuts;
• wake, wake, waken soya da sauran wake;
• Dill, Faski, Basil;
• farin gurasa.