Werner ta ciwo

Yarar wata hanya ce wanda ba zai iya jurewa ba wanda ke shafar kowane mutum, yana gudana cikin hankali da ci gaba. Duk da haka, akwai wata cuta wadda wannan tsari zai bunƙasa sosai, yana shafi dukkanin sassan da tsarin. Wannan cututtukan suna kira progeria (daga Girkanci - wanda bai tsufa ba), yana da wuya (1 yanayin ga mutane 4 zuwa 8), a kasarmu akwai wasu lokuta da yawa. Akwai manyan nau'i biyu na progeria: Hutchinson-Guilford ciwo (progeria of children) da kuma Werner ta ciwo (progeria na manya). Game da karshen za mu tattauna a cikin labarinmu.

Werner's Syndrome - asirin kimiyya

Werner ta ciwo yaron farko da likitan Jamus Otto Werner ya bayyana a cikin shekara ta 1904, amma har ya zuwa yanzu, kwayar cutar ta kasance mummunar cutar, musamman saboda abin da ya faru. An san cewa wannan mummunan cututtukan kwayoyin halitta ne da aka haifar da maye gurbi, wadda aka gaji.

A yau, masana kimiyya sun ƙaddara cewa cutar ciwon Werner ita ce cututtuka mai kwari. Wannan yana nufin cewa marasa lafiya tare da progeria sun karu daga lokaci guda daga mahaifin da mahaifiyar daya daga cikin kwayoyin halitta wanda aka samo a cikin takwas chromosome. Duk da haka, har yanzu bazai yiwuwa ya tabbatar ko ƙaryar ganewar asali ta hanyar binciken kwayoyin ba.

Dalilin dalilai na matakan girma

Babban dalilin ciwo na tsufa ba ya da kyau. Kwayoyin da aka cutar da su a cikin jigilar mahaifa na masu haƙuri da kwayar cutar ba su shafi jikin su ba, amma idan sun haɗu da kai zuwa mummunan sakamako, suna la'akari da yaro ga wahala a nan gaba da kuma tashi daga rayuwa. Amma abin da ke haifar da irin wannan maye gurbi ba shi da tabbas.

Cutar cututtuka da kuma irin wannan cuta

Harshen farko na ciwo na Werner yana faruwa tsakanin shekarun 14 da 18 (wani lokaci daga baya), bayan lokacin haihuwa. Har zuwa wannan lokaci, dukkan marasa lafiya sukan ci gaba da al'ada, kuma a cikin jiki zasu fara tafiyar da tsarin rayuwa. A matsayinka na mai mulki, a farkon marasa lafiya juya launin toka, wanda aka haɗuwa tare da gashin gashi. Akwai tsoffin canji a fata: bushewa, wrinkles , hyperpigmentation, fata tightening, kodadde.

Akwai nau'o'in pathologies masu yawa waɗanda ke biye da tsufa na tsofaffi: cataracts , atherosclerosis, cututtuka na zuciya da zuciya, osteoporosis, iri-iri iri-iri da kuma mummunan neoplasms.

Har ila yau ana lura da cututtuka na endocrine: ba tare da alamun jima'i na biyu da haila ba, bakararre, babban murya, rashin jin dadi, maganin ciwon sukari. Atrophy nama da tsokoki, makamai da ƙafafunsu sun zama maƙasudin ƙananan ƙwayar jiki, haɗarsu tana da iyakancewa.

An bayyana su da karfi mai sauƙi da siffofin fuska - suna nunawa, ƙwaƙwalwar ƙwaƙwalwa ce, hanci yana samun kama da tsuntsu, bakin ya rage. A shekarun shekaru 30 zuwa 30, mutumin da ke da girma a matsayin mai girma yana kama da mutum 80. Magunguna da ciwo na Werner sunyi rayuwa har zuwa shekaru 50, suna mutuwa yawanci daga ciwon daji, ciwon zuciya ko bugun jini.

Jiyya na progeria babba

Abin takaici, babu wata hanya ta kawar da wannan cuta. An yi amfani da magani ne kawai don kawar da bayyanar cututtuka, da kuma hana cututtuka masu kwantar da hankali da kuma ƙwarewarsu. Tare da ci gaba da tilasta filastik, yana yiwuwa a dan kadan ya gyara bayyanuwar waje na tsufa.

A halin yanzu, ana gudanar da gwaje-gwajen don maganin ciwo na Werner ta jikin kwayoyin jini. Har yanzu ana fatan za a samu sakamako masu kyau a nan gaba.