Ciwon granulomatosis na Wegener shine cututtukan fata wanda yake nufin cututtuka masu tsanani da sauri. Tsarin kwayoyin halitta da kuma Granglomatosis Wegener suna da alaka da cututtuka, saboda an riga an kafa antibodies (antineutrophil cytoplasmic) a cikin granulomatosis, wanda shine halayyar ANCA.
Dalili na granulomatosis na Wegener
Girbin granulomatosis na Wegener yana nufin autoimmune, saboda haka akwai wata kwayar halitta. A gaskiya ma, granulomatosis bai dace da amsawa ba. Don haka, alamun cutar sune antigens - HLA 添 B 批 _7, B_8, 非 DR 张 _2, 他〗 _w7.
Aikin pathogens kuma an yi amfani da kwayar cutar antineutrophil cytoplasmic dake amsawa da proteinase-3.
Girbin granulomatosis na Wegener - bayyanar cututtuka
Kwayoyin cututtuka na granulomatosis sau da yawa yakan faru a lokacin shekaru 40, yayin da jinsi ba shi da matsala.
Granulomatosis - ƙonewa na ganuwar ƙananan ƙananan matakan jirgin ruwa: kwari, capillaries, arteries da arterioles. A cikin tsarin shan kashi, sashen na numfashi na sama, kodan, idanu, huhu da sauran gabobin suna da hannu.
A bayyanar cututtuka sune kamar haka:
- general - asarar hasara, rauni, myalgia, arthralgia, zazzabi, a lokuta masu wuya, arthritis;
- tsarin jin tsoro - polyneuropathy asymmetric;
- idanu - ischemia na jijiya na gani, makanta, episcleritis tare da orbital granuloma da exophthalmos;
- fata - rashes da abubuwa necrotic;
- kodan - glomerulonephritis , wanda zai iya daukar hanya mai sauri;
- huhu - raunuka na ci gaba da kashi 75 cikin 100 na marasa lafiya a cikin nau'in infiltrates, wanda ke haifar da cavities a lokacin lalata; tare da wannan za a iya kiyaye pleurisy, tari.
- alamu na numfashi - sun shafi kashi 90 cikin 100 na marasa lafiya a cikin rhinitis tare da lalacewa da halayen ƙwayar cuta; Tsinkayar ƙananan nasus yana haifar da lalatawar sirri; Har ila yau, lagin na rinjayar larynx, kunnuwa, trachea, sinadaran paranasal, wanda aka lura da tsarin necrotic.
Ciwon granulomatosis na Wegener yana da nau'i biyu:
- yanci - yana rinjayar magungunan na numfashi na sama;
- an gama shi - tare da jikinta da yawa, kuma wannan yana tare da zazzabi, ciwon haɗin gwiwa, tsoka da ƙetare zuciya.
Binciken asalin granulomatosis na Wegener
Wannan ganewar asali ne wanda masanin ilimin lissafi ya samo asali bisa bayanan da yawa:
- gwaje-gwaje na jini - biochemical da general, wanda ba zai iya tabbatar da granulomatosis, amma taimako ya yi sarauta daga wasu cututtuka;
- bincike na gaggawa - yana iya tabbatarwa ko kuma cire cutarwa na koda (irin wannan cuta ya ƙaddara);
- X-ray na sinus da nau'i na paranasal (lissafin lissafi da aka lissafa ya ba da cikakken bayani fiye da wanda X-ray ya samu);
- biopsy - kadai hanya da ta tabbatar da tabbatarwa ko ƙaryar gaban granulomatosis; likitoci sun cire nama daga hanci ko ƙuru, kuma a wasu lokuta, kodan da kuma huhu.
Jiyya na granulomatosis na Wegener
An yi maganin cutar, musamman, tare da sanya corticosteroids da cytostatics, wanda ya rage aiki
Tare da lalacewar koda mai tsanani, a wasu lokuta, mai haƙuri yana buƙatar safarar jikin.
Girbin granulomatosis na Wegener - ganewa
Idan ba a fara samun magani ba a lokacin da ya dace, to, rashin ganewa ba zai yiwu ba a cikin watanni 6-12, kuma yawancin rai ba zai wuce watanni 5 ba.
Idan akwai magani, gyaran yana da shekaru 4, a wasu lokuta shekaru 10. Cikakken magani a halin yanzu na cigaban maganin ba zai yiwu ba.